An almost always malignant GLUCAGON-secreting tumor derived from the PANCREATIC ALPHA CELLS. It is characterized by a distinctive migratory ERYTHEMA; WEIGHT LOSS; STOMATITIS; GLOSSITIS; DIABETES MELLITUS; hypoaminoacidemia; and normochromic normocytic ANEMIA.
Also Known As:
Glucagonoma Syndrome; Adenoma, alpha Cell; Adenomas, alpha-Cell; Glucagonoma Syndromes; Glucagonomas; Syndrome, Glucagonoma; Syndromes, Glucagonoma; Tumor, alpha-Cell; Tumors, alpha-Cell; alpha Cell Tumor; alpha-Cell Adenoma; alpha-Cell Adenomas; alpha-Cell Tumors; Adenoma, alpha-Cell; alpha-Cell Tumor