Arrhythmic manifestation in β-thalassemia cardiomyopathy: a complex management.

Abstract

A young male with β-thalassemia major was implanted with a single-chamber Implantable cardioverter-defibrillator (ICD) for a cardiac arrest due to ventricular fibrillation. He received multiple inappropriate shocks due to atrioventricular nodal re-entrant tachycardia (AVNRT) treated with radiofrequency catheter ablation and then to high-rate atrial tachycardia refractory to amiodarone and not inducible during electrophysiological study. He refused empirical pulmonary vein isolation. Upgrading to biventricular ICD and performing atrioventricular node ablation avoided further inappropriate shocks.

• Authors: Enrico Chieffo, Matteo Astuti, Silvia Pica, Maurizio Eugenio Landolina
• Journal: Journal of cardiovascular medicine (Hagerstown, Md.) (J Cardiovasc Med (Hagerstown)) Vol. 22 Issue 12 Pg. e41-e42 (Dec 01 2021) ISSN: 1558-2035 [Electronic] United States
• PMID: 34570035 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright © 2021 Italian Federation of Cardiology - I.F.C. All rights reserved.

Topics

• Adult
• Atrioventricular Node (physiopathology, surgery)
• Blood Transfusion (methods)
• Catheter Ablation (methods)
• Defibrillators, Implantable (adverse effects)
• Humans
• Hypertrophy, Left Ventricular (diagnostic imaging, etiology, physiopathology)
• Iron Overload (diagnosis, etiology)
• Magnetic Resonance Imaging, Cine (methods)
• Male
• Tachycardia, Supraventricular (etiology, physiopathology, therapy)
• Treatment Outcome
• beta-Thalassemia (complications, therapy)