Abstract |
We describe a previously symptom-free 13-year-old boy with dominant partial interferon-γ receptor-1 deficiency and unusual varicella-zoster virus reactivation. This case supports the unsettled notion that some interferon-γ R-deficient patients are at enhanced risk for viral disease.
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Authors | Joachim Roesler, Christian Hedrich, Martin W Laass, Klaus Heyne, Angela Rösen-Wolff |
Journal | The Pediatric infectious disease journal
(Pediatr Infect Dis J)
Vol. 30
Issue 3
Pg. 265-6
(Mar 2011)
ISSN: 1532-0987 [Electronic] United States |
PMID | 20842068
(Publication Type: Case Reports, Journal Article)
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Chemical References |
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Topics |
- Adolescent
- Encephalitis, Varicella Zoster
(diagnosis, virology)
- Herpesvirus 3, Human
(isolation & purification)
- Humans
- Immunologic Deficiency Syndromes
(complications)
- Male
- Meningoencephalitis
(diagnosis, virology)
- Receptors, Interferon
(deficiency)
- Virus Activation
- Interferon gamma Receptor
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