Respiratory muscle weakness is often complicated in patients with
heart failure. Its presence further worsens the
clinical course of
heart failure. However, the effect and appropriate method of inspiratory muscle training has not previously been elucidated. A 55-year-old man with
dilated cardiomyopathy was admitted for intractable
heart failure. His
heart failure was dependent on
catecholamine infusion and the implantation of left
ventricular assist device was planned. He also had suffered from some
muscle weakness, which was later diagnosed as
lamin dystrophy due to mutation of LMNA c.G97T E33X. Preoperatively we started aerobic rehabilitation with inspiratory muscle training. Before training, inspiratory and expiratory muscle strength was significantly reduced and exercise capacity was decreased. The load of inspiratory training could be gradually increased along the result of regular evaluation of respiratory muscle strength. During 8 weeks of training, there was no worsening of
heart failure and no significant events related to
arrhythmia. After
training, respiratory muscle strength and exercise capacity were improved significantly. <Learning objective: Inspiratory muscle training was effective and safe in a patient with intractable
heart failure, which was complicated by skeletal muscle
myopathy due to
lamin-related
muscular dystrophy.>.