Clinical Features of Genetic Cardiac Diseases Related to Potassium Channelopathies.

Abstract

Genetic cardiac diseases related to potassium channelopathies are a group of relatively rare syndromes that includes long QT syndrome, short QT syndrome, Brugada syndrome, and early repolarization syndrome. Patients with these syndromes share a propensity for the development of life-threatening ventricular arrhythmias in the absence of significant cardiac structural abnormalities. Familial atrial fibrillation has also been associated with potassium channel dysfunction but differs from the other syndromes by being a rare cause of a common condition. This article focuses on the clinical features, diagnosis, and management of these syndromes.

• Authors: Arnon Adler, Sami Viskin
• Journal: Cardiac electrophysiology clinics (Card Electrophysiol Clin) Vol. 8 Issue 2 Pg. 361-72 (06 2016) ISSN: 1877-9190 [Electronic] United States
• PMID: 27261827 (Publication Type: Journal Article, Review)
• Copyright: Copyright © 2016 Elsevier Inc. All rights reserved.

Chemical References

• Potassium Channels

Topics

• Arrhythmias, Cardiac (diagnosis, genetics, physiopathology)
• Electrocardiography
• Humans
• Potassium Channels (genetics)