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Long QT Syndrome

A condition that is characterized by episodes of fainting (SYNCOPE) and varying degree of ventricular arrhythmia as indicated by the prolonged QT interval. The inherited forms are caused by mutation of genes encoding cardiac ion channel proteins. The two major forms are ROMANO-WARD SYNDROME and JERVELL-LANGE NIELSEN SYNDROME.
Also Known As:
Electrocardiogram QT Prolonged
Networked: 1833 relevant articles (40 outcomes, 98 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Torsades de Pointes (Torsade de Pointes)
2. Syncope (Fainting)
3. Ventricular Tachycardia
4. Cardiac Sudden Death (Sudden Cardiac Arrest)
5. Polymorphic catecholergic ventricular tachycardia

Experts

1. Ackerman, Michael J: 120 articles (10/2022 - 03/2002)
2. Tester, David J: 47 articles (01/2022 - 05/2002)
3. Wilde, Arthur A M: 39 articles (01/2022 - 02/2002)
4. Zareba, Wojciech: 35 articles (01/2022 - 01/2002)
5. Shimizu, Wataru: 34 articles (01/2022 - 02/2002)
6. Moss, Arthur J: 33 articles (02/2019 - 01/2002)
7. Schwartz, Peter J: 32 articles (01/2022 - 02/2002)
8. McNitt, Scott: 26 articles (01/2022 - 01/2007)
9. Bos, J Martijn: 25 articles (10/2022 - 09/2011)
10. Roden, Dan M: 24 articles (01/2022 - 03/2002)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Long QT Syndrome:
1. Ion Channels (Ion Channel)IBA
2. Sodium Channels (Sodium Channel)IBA
3. Mexiletine (Mexitil)FDA LinkGeneric
4. Adrenergic beta-Antagonists (beta-Adrenergic Blocking Agents)IBA
5. Atenolol (Tenormin)FDA LinkGeneric
6. Potassium Channels (Potassium Channel)IBA
7. Anti-Arrhythmia AgentsIBA
8. DNA (Deoxyribonucleic Acid)IBA
9. MagnesiumIBA
10. Flecainide (Tambocor)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Sympathectomy (Sympathectomies)
3. Implantable Defibrillators (Implantable Cardioverter-Defibrillator)
4. Secondary Prevention
5. Precision Medicine