[A case of Marfan syndrome with recurrent bilateral pneumothorax and anuloaortic ectasia].

Abstract

A 17-year-old male patient with Marfan syndrome was admitted due to recurrent bilateral pneumothorax which had recurred totally 11 times during the past 3 years. For the treatment of obstinately continuing right pneumothorax resection of bullae in combination with pleuropexy using OK 432 was effective. Two months thereafter Bentall operation with a composite graft consisting of a woven Dacron tube and a Björk-Shiley 27 mm aortic valve prosthesis was performed for his anuloartic ectasia. Left pneumothorax recurred 2 weeks after Bentall operation. But it was treated successfully with OK 432 injection into the left pleural cavity. Now, he is doing well as a student.

• Authors: N Yoshimura, T Asada, H Matsuda, H Nohara, T Higami, M Nishiwaki, N Mukohara, M Chibana, K Ogawa
• Journal: Kyobu geka. The Japanese journal of thoracic surgery (Kyobu Geka) Vol. 43 Issue 2 Pg. 157-9 (Feb 1990) ISSN: 0021-5252 [Print] Japan
• PMID: 2308250 (Publication Type: Case Reports, English Abstract, Journal Article)

Chemical References

• Picibanil

Topics

• Aged
• Aortic Aneurysm (etiology, surgery)
• Blood Vessel Prosthesis
• Heart Valve Prosthesis
• Humans
• Male
• Marfan Syndrome (complications)
• Picibanil (therapeutic use)
• Pneumothorax (etiology)