A slowly progressive condition of unknown etiology, characterized by deposition of fibrous tissue in the retroperitoneal space compressing the ureters, great vessels, bile duct, and other structures. When associated with abdominal aortic aneurysm, it may be called chronic periaortitis or inflammatory perianeurysmal fibrosis.
Also Known As:
Fibrosis, Inflammatory Perianeurysmal; Fibrosis, Perianeurysmal Inflammatory; Idiopathic Retroperitoneal Fibrosis; Inflammatory Fibrosis, Perianeurysmal; Inflammatory Perianeurysmal Fibrosis; Ormond's Disease; Perianeurysmal Inflammatory Fibrosis; Chronic Periaortitides; Chronic Periaortitis; Disease, Ormond; Disease, Ormond's; Fibroses, Retroperitoneal; Fibrosis, Retroperitoneal; Periaortitides, Chronic; Retroperitoneal Fibroses; Ormond Disease; Perianeurysmal Fibrosis, Inflammatory; Periaortitis, Chronic