Successful Prophylactic Endovascular Therapy for a Rapidly Expanding Hepatic Arterial Aneurysm in a Patient with Vascular Ehlers-Danlos Syndrome.

Abstract

Vascular Ehlers-Danlos syndrome (vEDS) causes fatal vascular complications due to vascular fragility. However, invasive therapeutic procedures are generally avoided except in emergencies. We report a case of vEDS presenting with rapid expansion of a hepatic arterial aneurysm successfully treated using prophylactic endovascular therapy. A 43-year-old woman with vEDS confirmed by genetic testing was hospitalized for a symptomatic hepatic arterial aneurysm that expanded rapidly within a week. Prophylactic coil embolization was then successfully performed. Although the general applicability of this approach cannot be determined, prophylactic endovascular therapy can clearly be an option for arterial aneurysms at high risk of rupture.

• Authors: Yukihiro Watanabe, Koichi Akutsu, Daisuke Yasui, Fumie Sugihara, Hideki Miyachi, Hiroshi Hayashi, Eiichiro Oka, Hidenori Komiyama, Shin-Ichiro Kumita, Wataru Shimizu
• Journal: Annals of vascular diseases (Ann Vasc Dis) Vol. 14 Issue 2 Pg. 163-167 (Jun 25 2021) ISSN: 1881-641X [Print] Japan
• PMID: 34239643 (Publication Type: Journal Article)
• Copyright: © 2021 The Editorial Committee of Annals of Vascular Diseases.