Successful management of anesthesia complications in a child with Crouzon syndrome.

Abstract

Crouzon syndrome (CS) is a rare autosomal dominant inherited disorder caused by mutations in the fibroblast growth factor receptor 2 (FGFR2) gene. The disease is characterized by premature fusion of the coronal and sagittal sutures of the skull, resulting in clinical manifestations of midfacial hypoplasia, shallow orbit, maxillary dysplasia, and occasional upper respiratory obstruction. This article presents the case of a child aged 2 years and 7 months with CS scheduled for bilateral tonsillectomy and adenoidectomy. The patient had a difficult procedure of extubation and was reintubated and the tracheal intubation was removed 2 days after surgery. The CS is a rare condition with physical characteristics that can result in difficult airway manipulation. It is important for anesthesiologists to recognize and avoid potential airway complications in the management of such patients through detailed preoperative evaluation and careful observation after surgery to reduce perioperative risks.

• Authors: X Wang, Z Xu, Y Xiao, G Chen
• Journal: Der Anaesthesist (Anaesthesist) Vol. 69 Issue 6 Pg. 432-435 (06 2020) ISSN: 1432-055X [Electronic] Germany
• Vernacular Title: Erfolgreiches Management von anästhesiologischen Komplikationen bei einem Kind mit Crouzon-Syndrom.
• PMID: 32377797 (Publication Type: Case Reports, Journal Article)

Topics

• Adenoidectomy
• Airway Extubation
• Airway Obstruction (etiology)
• Anesthesia (methods)
• Child, Preschool
• Craniofacial Dysostosis (complications, surgery)
• Humans
• Male
• Perioperative Care
• Tonsillectomy