A rare spontaneous osteosarcoma of the calvarium in a patient with long-standing fibrous dysplasia: CT and MR findings.

Abstract

A 52-year-old man with long-standing craniofacial polyostotic fibrous dysplasia (FD) and no history of prior radiation therapy developed a spontaneous right temporal bone osteosarcoma. Such spontaneous sarcomatous degeneration of FD is rare, particularly in the calvarium/skull, where, to our knowledge, only six prior cases have been reported in the literature. We report this case because it is a rare entity with well-documented CT and MR images, and to emphasize the importance of depicting imaging features of sarcomatous degeneration among the complex imaging findings of FD.

• Authors: C Reis, E M Genden, J B Bederson, P M Som
• Journal: The British journal of radiology (Br J Radiol) Vol. 81 Issue 962 Pg. e31-4 (Feb 2008) ISSN: 1748-880X [Electronic] England
• PMID: 18238909 (Publication Type: Case Reports, Journal Article)

Topics

• Facial Bones (abnormalities)
• Fibrous Dysplasia, Polyostotic (complications)
• Humans
• Magnetic Resonance Imaging
• Male
• Middle Aged
• Osteosarcoma (complications, diagnosis)
• Skull (abnormalities)
• Skull Neoplasms (complications, diagnosis)
• Temporal Bone
• Tomography, X-Ray Computed