Authors | D M Turnbull, K Bartlett, D L Stevens, K G Alberti, G J Gibson, M A Johnson, A J McCulloch, H S Sherratt |
Journal | The New England journal of medicine
(N Engl J Med)
Vol. 311
Issue 19
Pg. 1232-6
(Nov 08 1984)
ISSN: 0028-4793 [Print] United States |
PMID | 6493275
(Publication Type: Case Reports, Journal Article, Research Support, Non-U.S. Gov't)
|
Chemical References |
- Ketone Bodies
- Acyl-CoA Dehydrogenases
- Butyryl-CoA Dehydrogenase
- Carnitine
|
Topics |
- Acyl-CoA Dehydrogenases
(deficiency)
- Butyryl-CoA Dehydrogenase
- Carnitine
(deficiency, urine)
- Fasting
- Female
- Humans
- Ketone Bodies
(metabolism)
- Lipid Metabolism, Inborn Errors
(metabolism, pathology)
- Middle Aged
- Mitochondria, Muscle
(enzymology)
- Muscles
(metabolism, ultrastructure)
- Muscular Diseases
(metabolism, pathology)
- Physical Exertion
- Respiration
|