Heart transplant anesthetic approach in a patient with Emery Dreyfuss muscular dystrophy: A case report.

Abstract

Emery-Dreifuss muscular dystrophy is associated with cardiac abnormalities and rarely heart transplantation may be the treatment of choice. In this case, a male patient with Emery- Dreifuss muscular dystrophy developed NYHA class IV heart failure at 33 years of age and was submitted to heart transplantation. Anesthesia was adapted to prevent the development of malignant hyperthermia and rhabdomyolysis. The surgery was a success and the patient's progress was extremely positive with symptomatic improvement. In these patients, is critical to adjust not only his positioning but also the therapy administered in order to reduce iatrogeny and promote a faster recovery.

• Authors: I Q Martins, M Cuervo, I Vilhena
• Journal: Revista espanola de anestesiologia y reanimacion (Rev Esp Anestesiol Reanim (Engl Ed)) Vol. 70 Issue 9 Pg. 540-544 (11 2023) ISSN: 2341-1929 [Electronic] Spain
• PMID: 37678464 (Publication Type: Case Reports)
• Copyright: Copyright © 2022 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Publicado por Elsevier España, S.L.U. All rights reserved.

Chemical References

• Anesthetics

Topics

• Humans
• Male
• Muscular Dystrophies (complications)
• Muscular Dystrophy, Emery-Dreifuss (complications, therapy)
• Anesthesia
• Heart Transplantation
• Anesthetics