Airway Management in a Patient with Wolf-Hirschhorn Syndrome.

Abstract

We present a case of a 3-month-old female with Wolf-Hirschhorn syndrome (WHS) undergoing general anesthesia for laparoscopic gastrostomy tube placement with a focus on airway management. WHS is a rare 4p microdeletion syndrome resulting in multiple congenital abnormalities, including craniofacial deformities. Microcephaly, micrognathia, and glossoptosis are common features in WHS patients and risk factors for a pediatric airway that is potentially difficult to intubate. We discuss anesthesia strategies for airway preparation and management in a WHS patient requiring general anesthesia with endotracheal intubation.

• Authors: John F Gamble, Dinesh J Kurian, Andrea G Udani, Nathaniel H Greene
• Journal: Case reports in pediatrics (Case Rep Pediatr) Vol. 2016 Pg. 7070125 ( 2016) ISSN: 2090-6803 [Print] United States
• PMID: 27752382 (Publication Type: Journal Article)