Cystoid macular edema secondary to gyrate atrophy in a child treated with sub-tenon injection of triamcinolone acetonide.

Abstract

Purpose: Gyrate atrophy (GA) of the fundus is a rare, progressive metabolic disease secondary to the deficiency of the pyridoxal phosphate-dependent enzyme, ornithine aminotransferase. GA may lead to cystoid macular edema (CME) resulting from chronic inflammation. We aimed to report a child case with CME secondary to gyrate atrophy. Methods: Herein we presented a GA case treated with posterior sub-Tenon triamcinolone acetonide injection. Results: Optical coherence tomography examination revealed the disappearance of the macular edema that is a vision-threatening complication in GA. Conclusion: The present case showed that the posterior sub-Tenon injection of long acting steroids might be a promising treatment in CME secondary to GA.

• Authors: Şahin Alparslan, Mehmet Türkcü Fatih, Şahin Muhammed, Yıldırım Adnan
• Journal: Romanian journal of ophthalmology (Rom J Ophthalmol) 2018 Jul-Sep Vol. 62 Issue 3 Pg. 246-249 ISSN: 2457-4325 [Print] Romania
• PMID: 30505995 (Publication Type: Case Reports, Journal Article)

Chemical References

• Glucocorticoids
• Triamcinolone Acetonide

Topics

• Adolescent
• Female
• Glucocorticoids (administration & dosage)
• Gyrate Atrophy (drug therapy)
• Humans
• Macular Edema (drug therapy)
• Tomography, Optical Coherence
• Treatment Outcome
• Triamcinolone Acetonide (administration & dosage)
• Vitreous Body