Abstract |
A 20-year-old man with severe physical weakness (from which he soon recovered spontaneously) was found to have hypoproteinaemia and lymphocytopenia (768/microliters). Ten years later, after having been free of symptoms in the meantime, oedema, ascites and abdominal pain occurred, associated with loss of physical capacity. Enteric loss of protein ( alpha 1-antitrypsin clearance increased about thirtyfold) with a total serum protein concentration of only 3.7 g/dl, as well as histological evidence of lymphangiectasia of the small and large intestines provided the diagnosis of primary intestinal lymphangiectasia. In the course of the disease cholelithiasis and ( after treatment with tranexamic acid) thrombosis of the axillary vein occurred. No treatment has been of any avail and the patient has been unable to work for three years.
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Authors | J Biermann, J Meinshausen, U Kuhlmann |
Journal | Deutsche medizinische Wochenschrift (1946)
(Dtsch Med Wochenschr)
Vol. 116
Issue 39
Pg. 1473-6
(Sep 27 1991)
ISSN: 0012-0472 [Print] Germany |
Vernacular Title | Therapierefraktäre primäre intestinale Lymphangiektasie. |
PMID | 1914911
(Publication Type: Case Reports, English Abstract, Journal Article)
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Chemical References |
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Topics |
- Adult
- Biopsy
- Blood Proteins
(analysis)
- Chronic Disease
- Diagnosis, Differential
- Humans
- Hypoproteinemia
(blood, pathology, therapy)
- Intestine, Small
(pathology)
- Lymphangiectasis, Intestinal
(blood, pathology, therapy)
- Lymphopenia
(blood, pathology, therapy)
- Male
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