Abstract | CONCLUSIONS:
Hearing loss and equilibrium dysfunction have different etiologies in patients with large vestibular aqueduct syndrome. We suggest that all children with distal renal tubular acidosis ( dRTA) should be subjected to an equilibrium study and audiological evaluation, as well as to a CT or MRI scan. OBJECTIVE:
dRTA has been described in association with sensorineural hearing loss, but there are no reported cases that have been examined in detail using audiological and equilibrium studies. We report here a case of progressive sensorineural hearing loss with a large vestibular aqueduct and dRTA, and the results of audiological and equilibrium studies. MATERIAL AND METHODS: RESULTS: The pure-tone audiogram of the patient was off the scale for the right ear and showed progressive sensorineural hearing loss for the left ear. Ice-water caloric testing showed canal paresis on the left side. Temporal bone CT and inner ear MRI revealed a large vestibular aqueduct and a large endolymphatic sac on both sides.
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Authors | Yukiko Shinjo, Kimitaka Kaga, Takashi Igarashi |
Journal | Acta oto-laryngologica
(Acta Otolaryngol)
Vol. 125
Issue 6
Pg. 667-70
(Jun 2005)
ISSN: 0001-6489 [Print] England |
PMID | 16076719
(Publication Type: Case Reports, Journal Article)
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Topics |
- Acidosis, Renal Tubular
(complications)
- Adult
- Audiometry, Pure-Tone
- Caloric Tests
(methods)
- Endolymphatic Sac
(abnormalities, diagnostic imaging)
- Female
- Follow-Up Studies
- Hearing Loss, Sensorineural
(etiology)
- Humans
- Semicircular Canals
(physiopathology)
- Temporal Bone
(diagnostic imaging)
- Tinnitus
(etiology)
- Tomography, X-Ray Computed
- Vertigo
(etiology)
- Vestibular Aqueduct
(abnormalities, diagnostic imaging)
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