A condition marked by recurrent seizures that occur during the first 4-6 weeks of life despite an otherwise benign neonatal course. Autosomal dominant familial and sporadic forms have been identified. Seizures generally consist of brief episodes of tonic posturing and other movements, apnea, eye deviations, and blood pressure fluctuations. These tend to remit after the 6th week of life. The risk of developing epilepsy at an older age is moderately increased in the familial form of this disorder. (Neurologia 1996 Feb;11(2):51-5)
Also Known As:
Benign Familial Neonatal Convulsions; Epilepsy, Benign Neonatal; Benign Familial Infantile Convulsions; Benign Familial Infantile Convulsions Syndrome; Benign Familial Neonatal Epilepsy; Benign Familial Neonatal-Infantile Seizures; Benign Infantile Familial Convulsions; Benign Neonatal Convulsions; Benign Neonatal Epilepsy, Nonfamilial; Benign Neonatal Non-Familial Convulsions; Benign Neonatal Nonfamilial Epilepsy; Benign Non-Familial Neonatal Convulsions; Convulsions Benign Familial Neonatal; Convulsions, Benign Familial Infantile, 1; Convulsions, Benign Familial Infantile, 3; Convulsions, Benign Neonatal, Familial; Convulsions, Benign Neonatal, Non-Familial; Epilepsy, Benign Neonatal, Familial; Epilepsy, Benign Neonatal, Non-Familial; Epilepsy, Benign Neonatal, Nonfamilial; Epilepsy, Benign Neonatal-Infantile; Familial Benign Neonatal Convulsions; Familial Benign Neonatal Epilepsy; Non-Familial Benign Neonatal Convulsions; Non-Familial Benign Neonatal Epilepsy; Seizures, Benign Familial Infantile, 1; Seizures, Benign Familial Infantile, 3; Seizures, Benign Familial Neonatal-Infantile; Benign Familial Neonatal Infantile Seizures; Benign Neonatal Convulsion; Benign Neonatal Epilepsies; Benign Neonatal Non Familial Convulsions; Benign Neonatal-Infantile Epilepsies; Benign Neonatal-Infantile Epilepsy; Benign Non Familial Neonatal Convulsions; Convulsion, Benign Neonatal; Convulsions, Benign Neonatal; Epilepsies, Benign Neonatal; Epilepsies, Benign Neonatal-Infantile; Epilepsy, Benign Neonatal Infantile; Neonatal Convulsion, Benign; Neonatal Epilepsies, Benign; Neonatal Epilepsy, Benign; Neonatal-Infantile Epilepsies, Benign; Neonatal-Infantile Epilepsy, Benign; Non Familial Benign Neonatal Convulsions; Non Familial Benign Neonatal Epilepsy; Seizures, Benign Familial Neonatal Infantile; Neonatal Convulsions, Benign