Abstract | INTRODUCTION:
Pycnodysostosis is a rare autosomal recessive syndrome that provides the abnormal bone metabolism that increases the susceptibility of patients to develop osteomyelitis. OBJECTIVE: This systematic review was conducted to analyze the risk factors associated with the development of complications in the jaws (fractures and osteomyelitis), as well as their clinical-pathological characteristics and therapeutic approaches in patients with pycnodysostosis. METHODS: Searches were performed in the PubMed, Web of Science, Scopus, Lilacs, and Cochrane databases. Case reports or case series that met the eligibility criteria according to the PRISMA statement were included. The full texts of 31 articles were retrieved. Twenty of these articles published between 1969 and 2018 were selected, which described 26 cases of osteomyelitis in patients with pycnodysostosis. RESULTS: CONCLUSION:
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Authors | Glória Maria de França, Fernanda Aragão Felix, Everton Freitas de Morais, Maurília Raquel de Souto Medeiros, Ana Cláudia de Macedo Andrade, Hébel Cavalcanti Galvão |
Journal | Brazilian journal of otorhinolaryngology
(Braz J Otorhinolaryngol)
2021 Sep-Oct
Vol. 87
Issue 5
Pg. 620-628
ISSN: 1808-8686 [Electronic] Brazil |
PMID | 33579598
(Publication Type: Journal Article, Review, Systematic Review)
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Copyright | Copyright © 2021 Associação Brasileira de Otorrinolaringologia e Cirurgia Cérvico-Facial. Published by Elsevier Editora Ltda. All rights reserved. |
Topics |
- Adult
- Female
- Humans
- Male
- Mandible
- Osteomyelitis
- Pycnodysostosis
(complications)
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