Basilar impression is a cranial base abnormality associated with
osteogenesis imperfecta (OI) with serious neurologic implications but controversial treatment options. Combined anterior and posterior
decompression with long-segment posterior fusion is often recommended. We report a patient with OI (Sillence type III) with
basilar impression treated with halo
traction followed by posterior surgery. The patient was a 12-year-old female with a presentation of
hiccups and change in upper extremity function. Diagnostic imaging revealed
syringomyelia, compensated
hydrocephalus,
basilar impression, and Chiari type I malformation. The patient was treated with halo
traction followed by posterior
decompression fusion from the occipital bone to C2. Bone fusion and improved syrinx were evident on images during the 5 years of follow-up. Five years after surgery, syrinx recurred and the fourth ventricular
catheter was revised. The treatment with halo
traction followed by posterior-only surgery of
basilar impression associated with OI resulted in a good postoperative outcome.