Atrioventricular septal defect with cor triatriatum: case report and review of the literature.

Abstract

Atrioventricular septal defect with cor triatriatum is a rare combination, with only nine cases reported so far. Cor triatriatum, a potentially correctable cause of pulmonary arterial hypertension in atrioventricular septal defect patients, was missed in a few earlier case reports, leading to death and subsequent diagnosis at autopsy. We report the case of 3-year-old female child with this combination (partial atrioventricular septal defect with cor triatriatum) wherein the final diagnosis was made at cardiac catheterization. Successful surgical correction was performed.

• Authors: A K Goel, A Saxena, S S Kothari
• Journal: Pediatric cardiology (Pediatr Cardiol) Vol. 19 Issue 3 Pg. 243-5 ( 1998) ISSN: 0172-0643 [Print] United States
• PMID: 9568222 (Publication Type: Case Reports, Journal Article, Review)

Topics

• Abnormalities, Multiple (diagnosis, surgery)
• Cardiac Catheterization
• Child, Preschool
• Cor Triatriatum (diagnosis, surgery)
• Echocardiography
• Electrocardiography
• Female
• Heart Septal Defects (diagnosis, surgery)
• Humans