Abstract |
The association of nevus flammeus with mongolian spot, nevus fuscoceruleus, nevus spilus and, with variable frequency, with nevus anemicus has been termed phacomatosis pigmentovascularis, a genodermatosis first described by Ota and co-workers. Four different combinations have been specified. Most cases are reported from the Japanese literature. Phacomatosis pigmentovascularis may constitute an exclusively cutaneous disorder, but overlapping with other syndromes like Klippel-Trenaunay syndrome or Sturge-Weber syndrome is also possible. We report a 30-year-old woman with nevus flammeus on the back and right arm associated with nevus fuscoceruleus on the back.
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Authors | W Achtelik, M Tronnier, H H Wolff |
Journal | Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete
(Hautarzt)
Vol. 48
Issue 9
Pg. 653-6
(Sep 1997)
ISSN: 0017-8470 [Print] Germany |
Vernacular Title | Kombinierter Naevus flammeus und Naevus fuscocoeruleus: Phacomatosis pigmentovascularis Typ IIa. |
PMID | 9410851
(Publication Type: Case Reports, English Abstract, Journal Article)
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Topics |
- Adult
- Biopsy
- Diagnosis, Differential
- Dysplastic Nevus Syndrome
(diagnosis, genetics, pathology)
- Female
- Hamartoma Syndrome, Multiple
(diagnosis, genetics, pathology)
- Humans
- Melanocytes
(pathology)
- Microscopy, Electron
- Nevus of Ota
(genetics)
- Phagocytes
(pathology)
- Skin
(pathology)
- Skin Neoplasms
(diagnosis, genetics, pathology)
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