Relationship between lower-lip fistulae and cleft lip and/or palate in Von der Woude syndrome.

Abstract

OBJECTIVE:

This study was conducted to evaluate the relationship between fistulae of the lower lip and cleft lip and/or palate in patients with Van der Woude syndrome.

METHODS:

The medical records of 11,000 patients with cleft lip and/or palate registered at the Cleft Lip-Palate Research and Rehabilitation Hospital, University of São Paulo, Bauru were reviewed. Of these patients, 133 (1.2%) presented with Van der Woude syndrome.

RESULTS:

Of the 133 patients, 88 (66.2%) exhibited full clefts, 22 (16.5%) only cleft lip, and 23 (17.3%) only cleft palate. The lower-lip fistulae observed in these 133 patients were bilateral symmetric in 66 (49.7%), bilateral asymmetric in 42 (31.6%), microform in 19 (14.3%), median in 5 (3.8%), and unilateral in 1 (0.7%).

CONCLUSION:

This population sample appears to exhibit the previously published tendency for bilateral, unilateral, or mixed-type congenital fistulae to be associated with cleft lip with or without cleft palate, while so-called microforms or conic elevations are almost exclusively associated with cleft palate.

• Authors: M A Onofre, H B Brosco, R Taga
• Journal: The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association (Cleft Palate Craniofac J) Vol. 34 Issue 3 Pg. 261-5 (May 1997) ISSN: 1055-6656 [Print] United States
• PMID: 9167079 (Publication Type: Journal Article)

Topics

• Child
• Cleft Lip
• Cleft Palate
• Female
• Fistula (congenital)
• Humans
• Lip Diseases (congenital)
• Male
• Salivary Gland Fistula (congenital)
• Syndrome