Progressive encephalomyelitis with rigidity responsive to plasmapheresis and immunosuppression.

Abstract

The stiff-man syndrome is reported in a 55-year-old woman who also had signs of severe bulbar musculature hypercontraction. These clinical features correspond to the progressive encephalomyelitis with rigidity syndrome. Diazepam was minimally beneficial, but after treatment with plasmapheresis and corticosteroids, she was still asymptomatic when seen 5 years later.

• Authors: L Fogan
• Journal: Annals of neurology (Ann Neurol) Vol. 40 Issue 3 Pg. 451-3 (Sep 1996) ISSN: 0364-5134 [Print] United States
• PMID: 8797535 (Publication Type: Case Reports, Journal Article)

Chemical References

• Adrenal Cortex Hormones

Topics

• Adrenal Cortex Hormones (therapeutic use)
• Disease Progression
• Encephalomyelitis (complications, physiopathology, therapy)
• Female
• Humans
• Immunosuppression Therapy
• Middle Aged
• Muscle Rigidity (etiology)
• Plasmapheresis