Management of ectopia lentis in a family with Marfan syndrome.

Abstract

OBJECTIVE:

To determine the effectiveness of combined pars plana vitrectomy-lensectomy and open-loop anterior chamber lens implantation for the management of ectopia lentis associated with Marfan syndrome.

METHODS:

Retrospective review of the medical records of 4 consecutive patients with Marfan syndrome who underwent combined pars plana lensectomy-vitrectomy and anterior chamber lens implantation at our institution between August 1994 and July 1995.

RESULTS:

All patients demonstrated postoperative visual acuity of 20/25 or better during an average follow-up period of 6 months (range, 4-9 months). Two patients developed pseudophakic pupillary block and required YAG laser iridotomy postoperatively.

CONCLUSIONS:

Pars plana lensectomy-vitrectomy and anterior chamber intraocular lens implantation appears to be an excellent technique for the management of ectopia lentis associated with Marfan syndrome. A bimanual, closed-system endosurgical technique avoids many of the complications previously associated with surgery for ectopia lentis.

• Authors: S B Koenig, W F Mieler
• Journal: Archives of ophthalmology (Chicago, Ill. : 1960) (Arch Ophthalmol) Vol. 114 Issue 9 Pg. 1058-61 (Sep 1996) ISSN: 0003-9950 [Print] United States
• PMID: 8790089 (Publication Type: Journal Article, Research Support, Non-U.S. Gov't)

Topics

• Adult
• Anterior Chamber (surgery)
• Ectopia Lentis (etiology, surgery)
• Family Health
• Humans
• Lens, Crystalline (surgery)
• Lenses, Intraocular
• Male
• Marfan Syndrome (complications)
• Middle Aged
• Postoperative Complications
• Retrospective Studies
• Visual Acuity
• Vitrectomy