Adrenocorticotropic hormone-secreting ganglioneuroblastoma associated with opsomyoclonic encephalopathy: a case report with immunohistochemical study.

Abstract

This report describes a case of a 3-year-old female with Cushing's syndrome associated with ganglioneuroblastoma and opsomyoclonic encephalopathy. Immunohistochemistry showed the tumor to be adrenocorticotropic hormone-secreting. At autopsy, a cerebellar degenerative lesion was also demonstrated.

• Authors: A Clerico, A Tenore, S Bartolozzi, D Remotti, L Ruco, C Dominici, E Properzi, M A Castello
• Journal: Medical and pediatric oncology (Med Pediatr Oncol) Vol. 21 Issue 9 Pg. 690-4 ( 1993) ISSN: 0098-1532 [Print] United States
• PMID: 8413006 (Publication Type: Case Reports, Journal Article)

Chemical References

• Adrenocorticotropic Hormone

Topics

• Adrenocorticotropic Hormone (metabolism)
• Brain Diseases (complications, pathology)
• Child, Preschool
• Cushing Syndrome (complications, pathology)
• Female
• Ganglioneuroblastoma (complications, metabolism, pathology)
• Humans
• Myoclonus (complications, pathology)
• Spinal Neoplasms (complications, metabolism, pathology)
• Thoracic Vertebrae (pathology)