Aim The aim of this report is to present a brief review of the current literature on the management of EEC. Case Report A term male neonate presented at birth with classic
bladder exstrophy, a variant of the exstrophy-
epispadias complex (EEC). The defect was covered with sterile
silicon gauzes and waterproof dressing; at 72 hours of life, primary closure without
osteotomy of bladder, pelvis, and abdominal wall was successfully performed. Discussion EEC incidence is approximately 2.15 per 1,00,000 live births; several urological, musculocutaneous, spinal, orthopedic, gastrointestinal, and gynecological anomalies may be associated to EEC. Initial medical management includes use of
occlusive dressings to prevent air contact and
dehydration of the open bladder template. Umbilical
catheters should not be positioned. Surgical repair stages include initial closure of the bladder and abdominal wall with or without
osteotomy, followed by
epispadias repair at 6 to 12 months, and bladder neck repair around 5 years of life. Those who fail to attain continence eventually undergo bladder augmentation and placement of a catheterizable conduit. Conclusion Modern-staged repair of EEC guarantees socially acceptable urinary continence in up to 80% of cases; sexual function can be an issue in the long term, but overall quality of life can be good.