Abstract | OBJECTIVES: STUDY DESIGN: Retrospective case review. SETTING: Tertiary referral center. PATIENTS: We reviewed medical charts of 367 cochlear implantation cases at Kyoto University Hospital between 1987 and 2012. We identified five patients with syndromic mitochondrial disease who underwent cochlear implantation surgery. The mean age of the patients (four women and one man) when they underwent surgeries was 44.4 years (range, 30-64 yr; median, 41 yr). INTERVENTIONS: Therapeutic and rehabilitative. MAIN OUTCOME MEASURE: In four of five patients, speech perception performance was measured using Japanese vowels, consonant-vowel syllables, and short sentences. RESULTS: Only 1.4% (5 of 367) of cochlear implantation cases at Kyoto University Hospital underwent cochlear implantation surgery because of syndromic mitochondrial diseases. Four of those patients showed significantly improved speech perception outcomes, and the beneficial effects of the intervention continued long after surgery. One patient could not perform speech perception test presumably because of poor cognitive function. CONCLUSION:
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Authors | Norio Yamamoto, Hideaki Okuyama, Harukazu Hiraumi, Tatsunori Sakamoto, Hitomi Matsuura, Juichi Ito |
Journal | Otology & neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
(Otol Neurotol)
Vol. 36
Issue 8
Pg. e129-33
(Sep 2015)
ISSN: 1537-4505 [Electronic] United States |
PMID | 26134938
(Publication Type: Journal Article, Research Support, Non-U.S. Gov't)
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Topics |
- Adult
- Cochlear Implantation
- Deafness
(etiology, surgery)
- Female
- Humans
- Male
- Middle Aged
- Mitochondrial Diseases
(complications)
- Retrospective Studies
- Speech Perception
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