Susac's syndrome: the value of fundus fluorescein angiography.

Abstract

A 19-year-old woman presented with a 4-week history of headache, ataxia, vertigo, confusion, intermittent blurred vision in the right eye and intermittent hearing loss. MRI revealed white matter lesions and 'pepper pot' lesions of the corpus callosum. The cerebrospinal fluid had raised protein and lymphocytes. Fundal examination revealed multiple peripheral arterial occlusions in the both eyes confirmed with fundus fluorescein angiography (FFA). A diagnosis of Susac's syndrome was made. The patient was initially treated with steroids, followed by azathioprine and intravenous immunoglobulins (IVIg). Clinical improvement was noted, associated with improvement of the retinal circulation on FFA.

• Authors: Imran Joseph Khan, Holger Allroggen, Sergio Pagliarini
• Journal: BMJ case reports (BMJ Case Rep) Vol. 2014 (Oct 03 2014) ISSN: 1757-790X [Electronic] England
• PMID: 25281252 (Publication Type: Case Reports, Journal Article)
• Copyright: 2014 BMJ Publishing Group Ltd.

Topics

• Brain (pathology)
• Female
• Fluorescein Angiography
• Fundus Oculi
• Humans
• Magnetic Resonance Imaging
• Retinal Artery Occlusion (diagnosis, etiology)
• Susac Syndrome (complications, diagnosis)
• Young Adult