[Anaesthetic implications in a pregnant patient with an extreme thrombocytopenia due to a May-Hegglin anomaly: general o regional anaesthesia?].

Abstract

The May-Hegglin anomaly is an inherited disorder, so uncommon that the incidence is still unknown. It is characterized by macro-thrombocytopenia with normal platelet function and cytoplasmic inclusion bodies in granulocytes. The case is reported of a 28-year-old primiparous patient who had an urgent caesarean section due to failed induction of labour. The patient had no history of abnormal bleeding. Other causes of thrombocytopenia or platelet dysfunction, such as preeclampsia, HELLP syndrome, or placental abruption, were ruled out. The platelet count prior to surgery was 20,900/mm(3) with normal platelet function. General anaesthesia was performed. No excessive bleeding occurred and a platelet transfusion was not needed.

• Authors: G García Vallejo, M Cabellos, M Kabiri, J R Fraile, J Cuesta
• Journal: Revista espanola de anestesiologia y reanimacion (Rev Esp Anestesiol Reanim) Vol. 61 Issue 8 Pg. 460-5 (Oct 2014) ISSN: 2340-3284 [Electronic] Spain
• Vernacular Title: Implicaciones anestésicas en gestante con trombocitopenia extrema por síndrome de May-Hegglin: ¿anestesia regional o general?
• PMID: 24704095 (Publication Type: Case Reports, Journal Article, Review)
• Copyright: Copyright © 2013 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Published by Elsevier España. All rights reserved.

Topics

• Adult
• Analgesia, Epidural
• Analgesia, Obstetrical (methods)
• Anesthesia, General (methods)
• Anesthesia, Obstetrical (methods)
• Cesarean Section
• Contraindications
• Emergencies
• Female
• Hearing Loss, Sensorineural (blood)
• Humans
• Platelet Count
• Pregnancy
• Pregnancy Complications, Hematologic (etiology)
• Thrombocytopenia (blood, congenital, etiology)