[Primary renal synovial sarcoma].

Abstract

The primary renal synovial sarcoma is a rare tumor with a poor prognosis. It may be confused with other types of mesenchymal kidney tumors because of similarities in clinical and histological appearance. About 60 cases have been described in the literature. We report a case of a 66-year-old man presenting a primary synovial sarcoma of the right kidney with a vascular invasion of the inferior vena cava and right renal vein. The diagnosis was confirmed in molecular biology by reverse transcription polymerase chain reaction (RT-PCR) which demonstrated a unique chromosomal translocation t(X;18) with SYT-SSX2 fusion transcripts. We describe here the case with a brief review.

• Authors: S Trolliet, V Lindner, S Krzisch, M Schneider, J L Jung
• Journal: Progres en urologie : journal de l'Association francaise d'urologie et de la Societe francaise d'urologie (Prog Urol) Vol. 24 Issue 3 Pg. 156-60 (Mar 2014) ISSN: 1166-7087 [Print] France
• Vernacular Title: Synovialosarcome rénal primitif.
• PMID: 24560202 (Publication Type: Case Reports, English Abstract, Journal Article, Review)
• Copyright: Copyright © 2013 Elsevier Masson SAS. All rights reserved.

Topics

• Aged
• Humans
• Kidney Neoplasms (pathology)
• Male
• Sarcoma, Synovial (pathology)