Congenital subclavian steal syndrome with multiple cerebellar infarctions caused by an atypical circumflex retroesophageal right aortic arch with atretic aberrant left subclavian artery.

Abstract

A right-sided aortic arch is a rare anomaly with an incidence of 0.1% worldwide and is usually associated with a mirror image of all supra-aortic branches or an aberrant left subclavian artery. The latter is often associated with a Kommerell diverticulum, although it can rarely be hypoplastic or atretic and lead to congenital subclavian steal. In most patients, the situation is well-tolerated. In this report, we present a case of subclavian steal syndrome with multiple cerebellar infarcts in a patient with an atypical right-sided aortic arch and an atretic aberrant left subclavian artery arising from a left-sided descending thoracic aorta.

• Authors: Apostolos T Mamopoulos, Bernd Luther
• Journal: Journal of vascular surgery (J Vasc Surg) Vol. 60 Issue 3 Pg. 776-9 (Sep 2014) ISSN: 1097-6809 [Electronic] United States
• PMID: 23958067 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright © 2014 Society for Vascular Surgery. Published by Mosby, Inc. All rights reserved.

Topics

• Aneurysm (complications, diagnosis, surgery)
• Aorta, Thoracic (abnormalities)
• Aortography (methods)
• Cardiovascular Abnormalities (complications, diagnosis, surgery)
• Cerebral Angiography (methods)
• Cerebral Infarction (diagnosis, etiology)
• Deglutition Disorders (complications, diagnosis, surgery)
• Humans
• Magnetic Resonance Angiography
• Male
• Middle Aged
• Subclavian Artery (abnormalities, surgery)
• Subclavian Steal Syndrome (diagnosis, etiology, surgery)
• Tomography, X-Ray Computed
• Treatment Outcome