Epithelioid PEComa (epithelioid angiomyolipoma) of the kidney: a rare tumor subtype for patients presenting with an enhancing renal mass.

Abstract

Epithelioid angiomyolipomas, or perivascular epithelioid cell tumors (epithelioid PEComas) of the kidney, are histologically related to renal angiomyolipomas (AMLs). However, in contrast to typical AMLs, this rare tumor can exhibit an aggressive clinical course with approximately 50% of reported cases demonstrating disease progression. In this report, we present a case of a 24-year-old female with a history of stone disease who was incidentally found to have a 9.0 cm right renal mass that was difficult to characterize radiographically preoperatively. The patient underwent a right radical nephrectomy, and pathology revealed a renal epithelioid PEComa.

• Authors: Adam B Shrewsberry, Gabriel L Sica, Adeboye O Osunkoya, Daniel J Canter
• Journal: The Canadian journal of urology (Can J Urol) Vol. 20 Issue 1 Pg. 6643-5 (Feb 2013) ISSN: 1195-9479 [Print] Canada
• PMID: 23433138 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Female
• Humans
• Incidental Findings
• Kidney Neoplasms (diagnosis, pathology, surgery)
• Magnetic Resonance Imaging
• Perivascular Epithelioid Cell Neoplasms (diagnosis, pathology, surgery)