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Huge desmoplastic fibroma of the paediatric mandible: surgical considerations and follow-up in three cases.

Abstract
The desmoplastic fibroma is a rare locally aggressive spindle-cell proliferation made up of fibroblasts/myofibroblasts immersed in a dense collagenic stroma. Head and neck localisation of desmoplastic fibromas is even more rare and the literature is limited to small case series and reviews. A comprehensive review of the English literature from 1968 to 2011 revealed only 79 cases of mandibular desmoplastic fibromas and only 18 (22%) in patients under 4 years of age. Complete resection with clear margins is the surgical first option, but it can be difficult to achieve in the paediatric mandible, especially for giant tumours as the three reported here. Mandibular reconstruction in these cases is mandatory to ensure correct craniofacial development. The authors present three cases of huge mandibular desmoplastic fibromas in paediatric patients treated with mandibulectomy and immediate reconstruction using rib grafts. Indications, reconstructive options and results are discussed.
AuthorsAndrea Ferri, Massimiliano Leporati, Domenico Corradi, Teore Ferri, Enrico Sesenna
JournalJournal of cranio-maxillo-facial surgery : official publication of the European Association for Cranio-Maxillo-Facial Surgery (J Craniomaxillofac Surg) Vol. 41 Issue 5 Pg. 367-70 (Jul 2013) ISSN: 1878-4119 [Electronic] Scotland
PMID23218503 (Publication Type: Case Reports, Journal Article)
CopyrightCopyright © 2012 European Association for Cranio-Maxillo-Facial Surgery. Published by Elsevier Ltd. All rights reserved.
Topics
  • Bone Plates
  • Bone Transplantation (methods)
  • Child, Preschool
  • Esthetics, Dental
  • Female
  • Fibroma, Desmoplastic (surgery)
  • Follow-Up Studies
  • Humans
  • Mandible (surgery)
  • Mandibular Condyle (surgery)
  • Mandibular Neoplasms (surgery)
  • Mandibular Reconstruction (methods)
  • Osteogenesis, Distraction (methods)
  • Range of Motion, Articular (physiology)
  • Reoperation
  • Ribs (transplantation)

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