[Effective epidural anesthesia for cesarean section in parturient woman with type I mucopolysaccharidosis (Hurler's syndrome)].

Abstract

Mucopolysaccharidosis is genetically determined disease caused by the deficiency of one of the lysosomal enzymes involved in the glycosaminoglycan (GAG) breakdown pathway. This metabolic block leads to the accumulation of GAG in various organs and tissues and affects nerve system, eyes, internal organs and musculoskeletal system. The reviewer of various articles on pubmed showed only one article about epidural anesthesia in patient with type I mucopolysaccharidosis. Our observation allows to consider that epidural anesthesia with ropivacaine is possible and safe in patients with type I mucopolysaccharidosis.

• Journal: Anesteziologiia i reanimatologiia (Anesteziol Reanimatol) 2011 Nov-Dec Issue 6 Pg. 29-31 ISSN: 0201-7563 [Print] Russia (Federation)
• PMID: 22379910 (Publication Type: Case Reports, Journal Article)

Chemical References

• Amides
• Anesthetics, Local
• Ropivacaine

Topics

• Adult
• Amides (administration & dosage, adverse effects)
• Anesthesia, Epidural (adverse effects, methods)
• Anesthesia, Obstetrical (adverse effects, methods)
• Anesthetics, Local (administration & dosage, adverse effects)
• Cesarean Section (methods)
• Female
• Humans
• Mucopolysaccharidosis I (complications)
• Pregnancy
• Pregnancy Complications
• Ropivacaine