[Good response of scleromyxedema and dermato-neuro syndrome to treatment with intravenous immunoglobulins].

Abstract

Scleromyxedema is a potentially serious disease that can have various systemic complications. One of the most frequent forms of central nervous system involvement is dermato-neuro syndrome. High-dose intravenous immunoglobulins are among the drug treatments that have been used for this syndrome. We describe 2 patients with scleromyxedema, one of whom developed dermato-neuro syndrome. Both patients responded well to treatment with high-dose intravenous immunoglobulins. We suggest this therapy as a suitable first-line treatment for scleromyxedema and for its neurological complications.

• Authors: I Bielsa, F Benvenutti, R M Guinovart, C Ferrándiz
• Journal: Actas dermo-sifiliograficas (Actas Dermosifiliogr) Vol. 103 Issue 4 Pg. 317-20 (May 2012) ISSN: 1578-2190 [Electronic] Spain
• Vernacular Title: Escleromixedema y síndrome dermato-neuro: buena respuesta al tratamiento con glucocorticoides e inmunoglobulinas endovenosas.
• PMID: 21917233 (Publication Type: Case Reports, English Abstract, Journal Article)
• Copyright: Copyright © 2011 Elsevier España, S.L. and AEDV. All rights reserved.

Chemical References

• Immunoglobulins, Intravenous

Topics

• Aged
• Female
• Humans
• Immunoglobulins, Intravenous (therapeutic use)
• Male
• Middle Aged
• Nervous System Diseases (drug therapy, etiology)
• Scleromyxedema (complications, drug therapy)
• Syndrome