Idiopathic portal hypertension during a catastrophic attack in a patient with primary antiphospholipid syndrome.

Abstract

A 43-year old male patient with hyponatremic hypertensive syndrome was diagnosed as catastrophic primary antiphospholipid syndrome (PAPS). He subsequently developed hepatosplenomegaly. The patient also carried thrombophilia- and haemochromatosis-associated gene mutations. Further investigations upon persistence of splenomegaly indicated development of idiopathic portal hypertension.

• Authors: M A Cikrikcioglu, H Erkal, M Hursitoglu, A Karadag, E Gundogan, S M Kayacan, T Tukek
• Journal: Acta gastro-enterologica Belgica (Acta Gastroenterol Belg) Vol. 73 Issue 4 Pg. 521-6 ( 2010) ISSN: 1784-3227 [Print] Belgium
• PMID: 21299166 (Publication Type: Case Reports, Journal Article)

Topics

• Acute Disease
• Adult
• Antiphospholipid Syndrome (complications, diagnosis, physiopathology)
• Humans
• Hypertension (complications)
• Hypertension, Portal (etiology)
• Hyponatremia (complications)
• Male
• Renal Artery Obstruction (complications)
• Splenomegaly (complications)
• Venous Thrombosis (complications)