Long-term outcome of large artificial patch aortic repair for diffuse stenosis in Williams syndrome.

Abstract

There have been only a few reports concerning the long-term results of a surgical procedure using a large artificial patch for patients with Williams syndrome. Twelve years have passed since a patient with William's syndrome underwent a surgery with a patch angioplasty for the diffuse supravalvular aortic stenosis and deformities of the neck branch arteries. The patient had a well-balanced aortic growth without stenotic or aneurysmal changes, which was confirmed during the time of the second surgery when replacing the mitral valve. This technique of using a large patch has proven to be safe for Williams syndrome patients with diffuse supravalvular aortic stenosis in the long term.

• Authors: Koichi Sughimoto, Yoshiharu Takahara, Kenji Mogi, Manabu Sakurai, Chikashi Aoki
• Journal: General thoracic and cardiovascular surgery (Gen Thorac Cardiovasc Surg) Vol. 58 Issue 10 Pg. 528-30 (Oct 2010) ISSN: 1863-6713 [Electronic] Japan
• PMID: 20941567 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Aorta (growth & development, surgery)
• Aortic Stenosis, Supravalvular (genetics, surgery)
• Aortography (methods)
• Arteries (abnormalities, surgery)
• Blood Vessel Prosthesis
• Blood Vessel Prosthesis Implantation (instrumentation)
• Constriction, Pathologic
• Heart Valve Prosthesis Implantation
• Humans
• Male
• Mitral Valve Insufficiency (surgery)
• Neck (blood supply)
• Prosthesis Design
• Time Factors
• Tomography, X-Ray Computed
• Treatment Outcome
• Williams Syndrome (genetics, surgery)