Long-term follow-up of a child with idiopathic restrictive cardiomyopathy.

Abstract

A ten-year-old male with palpebral edema was proved to have a restrictive hemodynamic pattern by cardiac catheterization. Sequential echocardiographic examination revealed uniformly depressed left ventricular diastolic properties, well-maintained left ventricular systolic function, and a progression of obliterative change of the left ventricular cavity. Myocardial biopsy at 17 years of age disclosed a normal endocardium and marked interstitial fibrosis of the myocardium. Consequently, a decrease of cardiac output and a marked biatrial enlargement have developed in association with persistent atrial fibrillation.

• Authors: A Miyazaki, F Ichida, Y Suzuki, T Okada
• Journal: Heart and vessels. Supplement (Heart Vessels Suppl) Vol. 5 Pg. 74-6 ( 1990) ISSN: 0935-736X [Print] Japan
• PMID: 2093719 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Atrial Fibrillation (complications, pathology)
• Biopsy
• Cardiomyopathy, Restrictive (complications, pathology, physiopathology)
• Child
• Echocardiography
• Endomyocardial Fibrosis (complications, pathology)
• Follow-Up Studies
• Humans
• Male
• Time Factors