Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report.

Abstract

Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.

• Authors: Lakshminarsimhaiah Geetha, Muthuchellappan Radhakrishnan, Biligiri Sridhar Raghavendra, G S Umamaheswara Rao, Bhagavatula Indira Devi
• Journal: Journal of anesthesia (J Anesth) Vol. 24 Issue 4 Pg. 594-7 (Aug 2010) ISSN: 1438-8359 [Electronic] Japan
• PMID: 20517622 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Anesthesia (methods)
• Decompression, Surgical
• Female
• Foramen Magnum (surgery)
• Humans
• Lung (physiopathology)
• Mucopolysaccharidosis IV (complications, physiopathology)