[Exceptional digestive location of crystal deposits in primary hyperoxaluria].

Abstract

We report 3 cases of primary oxalosis with nephrocalcinosis and severe renal failure. Extrarenal involvement was noted in bones in 3 cases, the heart in 2 cases, the central nervous system in 2 cases, the skin in 1 case and the eye in 1 case. The 3 patients presented with acute digestive disorders. Ultrasonography and CT scans showed digestive wall calcifications in addition to the classic appearance of primary oxalosis such as nephrocalcinosis or bone involvement. Primary hyperoxaluria is characterized by a calcium deposit in different tissues, mainly in kidneys. Digestive wall involvement has never been reported in the literature. Primary oxaluria should be considered in the presence of such a deposit in the gut wall.

• Authors: I Hasni Bouraoui, W Hajlaoui, H Jemni, N Arifa, K Mrad Dali, A Daadoucha, S Abroug, K Tlili Graeiss
• Journal: Archives de pediatrie : organe officiel de la Societe francaise de pediatrie (Arch Pediatr) Vol. 16 Issue 11 Pg. 1453-6 (Nov 2009) ISSN: 1769-664X [Electronic] France
• Vernacular Title: Localisation digestive exceptionnelle des dépôts cristallins dans l'hyperoxalurie primitive.
• PMID: 19747802 (Publication Type: Case Reports, English Abstract, Journal Article)

Chemical References

• Calcium Oxalate

Topics

• Abdominal Pain (etiology)
• Calcium Oxalate (metabolism)
• Child
• Digestive System (pathology)
• Digestive System Diseases (chemically induced)
• Female
• Humans
• Hyperoxaluria, Primary (diagnosis)
• Liver (pathology)
• Male
• Muscle, Smooth (pathology)
• Muscle, Smooth, Vascular (pathology)
• Nephrocalcinosis (diagnosis)
• Tomography, X-Ray Computed
• Ultrasonography
• Young Adult