[Surgical management of type II orbital neurofibromatosis].

Abstract

OBJECTIVE:

To study the clinical manifestations and surgical treatment of Type II orbital neurofibromatosis.

METHODS:

From Jan, 2001, to Oct, 2006, clinical data of 16 cases with type II orbital neurofibromatosis were retrospectively analyzed in the Department of Ophthalmology, Ninth People's Hospital, Medical School of Shanghai Jiao Tong University.

RESULTS:

All patients had orbito-temporal or intra-orbital neurofibromatosis, combined with periorbital deformities. After partial tumor resection, the orbital reconstruction and blepharoplasty were performed in the same stage. The patients were followed up for 6-12 months with no relapse. The vision was improved in 6 cases and kept the same in 10 cases. The cosmetic results were satisfactory in all cases. 5 cases were re-operated because of relapse of blepharoptosis.

CONCLUSIONS:

The function and appearance can be markedly improved after one-stage partial tumor resection, orbital reconstruction and blepharoplasty in patients with type II orbital neurofibromatosis.

• Authors: Ming Lin, Jin Li, Hui-fang Zhou, Yao Fu, Xian-Qun Fan
• Journal: Zhonghua zheng xing wai ke za zhi = Zhonghua zhengxing waike zazhi = Chinese journal of plastic surgery (Zhonghua Zheng Xing Wai Ke Za Zhi) Vol. 24 Issue 5 Pg. 347-9 (Sep 2008) ISSN: 1009-4598 [Print] China
• PMID: 19119632 (Publication Type: English Abstract, Journal Article)

Topics

• Adolescent
• Adult
• Female
• Follow-Up Studies
• Humans
• Male
• Neurofibromatosis 2 (surgery)
• Orbital Neoplasms (surgery)
• Plastic Surgery Procedures (methods)
• Retrospective Studies
• Young Adult