Optic nerve sheath fenestration for an isolated optic nerve glioma.

Abstract

The treatment modalities for neurofibromatosis type 1-associated optic gliomas include chemotherapy, radiation therapy, and surgical excision. The current recommendation is to consider treatment for an optic nerve glioma only if there is clear evidence of either ophthalmologic or radiographic progression with significant visual dysfunction. We report a case of a child with neurofibromatosis type 1 and an isolated optic nerve glioma with documented progression and visual loss in which clinical signs improved and visual deterioration stabilized after optic nerve sheath fenestration.

• Authors: Deborah K Vanderveen, Bharti R Nihalani, Philip Barron, Richard L Anderson
• Journal: Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus (J AAPOS) Vol. 13 Issue 1 Pg. 88-90 (Feb 2009) ISSN: 1528-3933 [Electronic] United States
• PMID: 18930671 (Publication Type: Case Reports, Journal Article)

Topics

• Female
• Glioma (pathology, surgery)
• Humans
• Infant
• Magnetic Resonance Imaging
• Neurofibromatosis 1 (pathology, surgery)
• Ophthalmologic Surgical Procedures
• Optic Nerve Neoplasms (pathology, surgery)