Conversion from total cavopulmonary shunt to Fontan circulation: improved cyanosis with an 11-year interval.

Abstract

We experienced a conversion case from total cavopulmonary shunt (TCPS) to the Fontan circulation with an 11-year interval in the left isomerism and an interruption of the inferior caval vein. Marked cyanosis (pulse oximetry measuring 74%) progressed 8 years after TCPS because of the prominent development of bilateral pulmonary arteriovenous fistula (PAVF), which was diminished after the Fontan conversion, and recent pulse oximetry measured 95% 22 months after the conversion. We believe that this report is a case with the longest interval from TCPS to Fontan in which PAVF was diminished and marked cyanosis was improved.

• Authors: Takeshi Hiramatsu, Shigeru Komori, Yoshiharu Nishimura, Yoshitaka Okamura, Hiroyuki Suzuki, Takashi Takeuchi
• Journal: Annals of thoracic and cardiovascular surgery : official journal of the Association of Thoracic and Cardiovascular Surgeons of Asia (Ann Thorac Cardiovasc Surg) Vol. 14 Issue 1 Pg. 29-31 (Feb 2008) ISSN: 1341-1098 [Print] Japan
• PMID: 18292737 (Publication Type: Case Reports, Journal Article)

Topics

• Child
• Cyanosis (prevention & control)
• Disease Progression
• Female
• Fontan Procedure
• Heart Bypass, Right
• Heart Defects, Congenital (surgery)
• Humans
• Oximetry