Kaposiform hemangioendothelioma: a rare cause of spontaneous hemothorax in infancy. Review of the literature.

Abstract

Kaposiform hemangioendothelioma is a rare vascular tumor found almost exclusively in early childhood often associated with a life-threatening thrombocytopenia and consumptive coagulopathy known as Kasabach-Merritt phenomenon. The natural history of these lesions and treatment remains controversial. We portray a case of a spontaneous hemothorax in a 2-month-old female infant and review of 153 reported cases in attempts to better delineate the available treatment options.

• Authors: Francisco Luis San Miguel, William Spurbeck, Carlos Budding, John Horton
• Journal: Journal of pediatric surgery (J Pediatr Surg) Vol. 43 Issue 1 Pg. e37-41 (Jan 2008) ISSN: 1531-5037 [Electronic] United States
• PMID: 18206444 (Publication Type: Case Reports, Journal Article, Review)

Topics

• Electrocoagulation (methods)
• Female
• Follow-Up Studies
• Hemangioendothelioma (complications, pathology, surgery)
• Hemothorax (diagnosis, etiology, surgery)
• Humans
• Infant
• Rare Diseases
• Risk Assessment
• Sarcoma, Kaposi (complications, pathology, surgery)
• Severity of Illness Index
• Thoracotomy (methods)
• Treatment Outcome
• Vascular Neoplasms (complications, pathology, surgery)