Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature.

Abstract

INTRODUCTION:

We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.

MATERIALS AND METHODS:

Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.

CONCLUSION:

In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.

• Authors: S J C Sammut, J Kandasamy, W Newman, A Sinha, J Ross, J C Blair, P May
• Journal: Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery (Childs Nerv Syst) Vol. 24 Issue 4 Pg. 515-20 (Apr 2008) ISSN: 0256-7040 [Print] Germany
• PMID: 18193400 (Publication Type: Case Reports, Journal Article, Review)

Topics

• Child
• Decompression, Surgical (methods)
• Female
• Fibrous Dysplasia, Polyostotic (complications, pathology, surgery)
• Humans
• Magnetic Resonance Imaging
• Optic Nerve (surgery)
• Pain (etiology, surgery)
• Tomography, X-Ray Computed
• Vision Disorders (etiology, surgery)
• Visual Acuity (physiology)
• Visual Fields (physiology)