[Rasmussen syndrome. Clinical study].

Abstract

Rasmussen's syndrome is a specific progressive disease affecting primarily one hemisphere, accompanied by intractable seizures and leading to severe neurologic and mental deficit. The authors present one child with frequent partial motor seizures and myoclonic seizures refractory to antiepileptic drug therapy who was diagnosed with epilepsia partialis continua. After a period of 15 months the patient develops a spastic right hemiparesis and mental degradation. Association of this signs of the clinical picture lead to the diagnostic of Rasmussen's syndrome who was confirmed by the presence of localized EEG abnormalities and imaging studies.

• Authors: Georgeta Diaconu, Ioana Grigore, M Burlea, Mariana Frasin
• Journal: Revista medico-chirurgicala a Societatii de Medici si Naturalisti din Iasi (Rev Med Chir Soc Med Nat Iasi) 2005 Jul-Sep Vol. 109 Issue 3 Pg. 511-5 ISSN: 0048-7848 [Print] Romania
• Vernacular Title: Sindromul Rasmussen. Studiu clinic.
• PMID: 16607742 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Brain (pathology, physiopathology)
• Child
• Electroencephalography
• Encephalitis (complications, diagnosis, pathology, physiopathology)
• Epilepsia Partialis Continua (etiology)
• Female
• Hemiplegia (etiology)
• Humans
• Intellectual Disability (etiology)
• Magnetic Resonance Imaging