[Congenital pseudarthrosis of the forearm in a neurofibromatosis patient: case report and review of the literature].

Abstract

We report a case of congenital pseudarthrosis of the forearm associated with neurofibromatosis type 1 which was treated by free vascularized periosteal flap transplant and repeated bone grafting. The young female patient recovered good hand and forearm function. A review of the literature revealed the rare occurrence of this disease (approximately 100 cases reported to date), which probably explains the wide variety of surgical proposals.

• Authors: R Kohler, F Solla, S Pinson, C Romana, E Chau, B Dohin
• Journal: Revue de chirurgie orthopedique et reparatrice de l'appareil moteur (Rev Chir Orthop Reparatrice Appar Mot) Vol. 91 Issue 8 Pg. 773-81 (Dec 2005) ISSN: 0035-1040 [Print] France
• Vernacular Title: Pseudarthrose congénitale de l'avant-bras associée à la neurofibromatose: à propos d'un cas et revue de la littérature.
• PMID: 16553000 (Publication Type: Case Reports, English Abstract, Journal Article, Review)

Topics

• Abnormalities, Multiple (surgery)
• Adolescent
• Female
• Humans
• Neurofibromatosis 1 (complications)
• Pseudarthrosis (complications, congenital, surgery)
• Radius (abnormalities, surgery)
• Ulna (abnormalities, surgery)