Pulmonary agenesis associated with dextrocardia, sternal defects, and ectopic kidney.

Abstract

Pulmonary agenesis is a rare embryological defect, usually unilateral, and is associated with skeletal, cardiovascular, and other anomalies. A 22-month-old girl was admitted to our clinic with recurrent pulmonary infections. A chest X-ray and multidetector computed tomography (MDCT) revealed pulmonary agenesis with dextrocardia, sternal defects, and a right pelvic ectopic kidney. We report on the first known case of right-sided pulmonary agenesis combined with isolated dextrocardia, sternal defects, and an ectopic kidney. The importance of MDCT for the diagnosis of pulmonary agenesis and associated other anomalies is demonstrated.

• Authors: Atilla Eroglu, Fatih Alper, Atila Turkyilmaz, Nurettin Karaoglanoglu, Adnan Okur
• Journal: Pediatric pulmonology (Pediatr Pulmonol) Vol. 40 Issue 6 Pg. 547-9 (Dec 2005) ISSN: 8755-6863 [Print] United States
• PMID: 16161099 (Publication Type: Case Reports, Journal Article)

Topics

• Dextrocardia (diagnostic imaging)
• Female
• Humans
• Infant
• Kidney (abnormalities, diagnostic imaging)
• Lung (abnormalities, diagnostic imaging)
• Pulmonary Artery (abnormalities, diagnostic imaging)
• Radiography
• Recurrence
• Respiratory Tract Infections (etiology)
• Sternum (abnormalities, diagnostic imaging)