Abstract | UNLABELLED: CONCLUSION:
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Authors | T M Cox |
Journal | Acta paediatrica (Oslo, Norway : 1992). Supplement
(Acta Paediatr Suppl)
Vol. 94
Issue 447
Pg. 69-75; discussion 57
(Mar 2005)
ISSN: 0803-5326 [Print] Norway |
PMID | 15895716
(Publication Type: Journal Article, Review)
|
Chemical References |
- Enzyme Inhibitors
- Glucosylceramides
- Glycosphingolipids
- 1-Deoxynojirimycin
- miglustat
- Glycoside Hydrolases
- Glucosylceramidase
- imiglucerase
|
Topics |
- 1-Deoxynojirimycin
(analogs & derivatives, therapeutic use)
- Enzyme Inhibitors
(therapeutic use)
- Glucosylceramidase
(metabolism)
- Glucosylceramides
(biosynthesis)
- Glycoside Hydrolases
(metabolism)
- Glycosphingolipids
(metabolism)
- Humans
- Lysosomal Storage Diseases
(metabolism, therapy)
- Substrate Specificity
|